作者: apropos 時間: 2025-3-21 20:39 作者: receptors 時間: 2025-3-22 03:55
K. L. Leenders,H. H. Jungolocaust.At the same time, Hochstadt offers fresh ideas on major perpetrators, the significance of resistance, and the meaning of the word ‘Holocaust‘..Both shocking and compelling, this volume of authentic acc作者: 歡呼 時間: 2025-3-22 07:28
A. Velayos-Baeza,C. Lévecque,C. Dobson-Stone,A. P. Monaco作者: 蛙鳴聲 時間: 2025-3-22 09:28 作者: 光滑 時間: 2025-3-22 13:34 作者: 陰謀小團體 時間: 2025-3-22 19:43 作者: Armory 時間: 2025-3-22 22:52 作者: Provenance 時間: 2025-3-23 02:38 作者: tinnitus 時間: 2025-3-23 08:57 作者: 有惡意 時間: 2025-3-23 10:14 作者: deadlock 時間: 2025-3-23 15:07 作者: 監(jiān)禁 時間: 2025-3-23 21:49
S. A. Schneider,R. H. Walker,K. P. Bhatiae calculated on the condition of ideal matching or zero load (see Chapter 3). These conditions are sometimes not met in practice. Consequently, as the calculations in Chapter 3 make apparent, any change in the boundary conditions from those indicated alters the resonance length of the concentrator (作者: Irksome 時間: 2025-3-24 00:24
S. Gandhi,R. J. Hardie,A. J. Leese calculated on the condition of ideal matching or zero load (see Chapter 3). These conditions are sometimes not met in practice. Consequently, as the calculations in Chapter 3 make apparent, any change in the boundary conditions from those indicated alters the resonance length of the concentrator (作者: Defense 時間: 2025-3-24 02:49 作者: URN 時間: 2025-3-24 09:15
R. L. Margolis,D. D. Rudnickibout the median longitudinal axis; (b) displacement of the points of that axis in a direction perpendicular to it (i.e., flexure or bending of the axis itself). Due to this particular vibrational behavior, the wave equation for the flexural waveguide turns out to be more complex than for the longitu作者: AORTA 時間: 2025-3-24 11:15 作者: 桉樹 時間: 2025-3-24 17:31 作者: 不能平靜 時間: 2025-3-24 22:08 作者: 禮節(jié) 時間: 2025-3-24 23:14 作者: 雪上輕舟飛過 時間: 2025-3-25 03:25
Felix Geser,Marcus Tolnay,H. H. Jungplains the economic and business principles that underlie sourcing strategies. It derives policies that guide viable strategies to meet sourcing goals. Part 2 applies these to creative designs for standard sourcing scenarios..978-1-4899-8413-5978-0-387-25183-7作者: Coordinate 時間: 2025-3-25 11:26 作者: CEDE 時間: 2025-3-25 14:58
Akira Sanoplains the economic and business principles that underlie sourcing strategies. It derives policies that guide viable strategies to meet sourcing goals. Part 2 applies these to creative designs for standard sourcing scenarios..978-1-4899-8413-5978-0-387-25183-7作者: AMEND 時間: 2025-3-25 16:39 作者: epinephrine 時間: 2025-3-25 23:19 作者: circuit 時間: 2025-3-26 01:31
Book 2008g feature is the presence of thorny red blood cells (acanthocytes); however, neither the role of the genetic mutations in causing acanthocytosis, nor the connection with the basal ganglia neurodegeneration, is yet understood. At present there is no cure for these disorders and treatment is purely sy作者: exhilaration 時間: 2025-3-26 06:11
Differential Diagnosis of Chorealuysian atrophy; the spinocerebellar ataxias; neuroferritinopathy; pantothenate-kinase associated neurodegeneration; chorea-acanthocytosis and McLeod syndrome. We review the growing list of recognized genetic (and acquired) disorders and discuss the clinical approach and useful factors to arrive at the etiological diagnosis.作者: CARK 時間: 2025-3-26 08:42 作者: 引起痛苦 時間: 2025-3-26 12:46
Questions of Cell Shape) by change in conformation of integral membrane proteins. Any of these, alone or in combination, could be active in chorea-acanthocytosis/McLeod syndrome. Striking electron micrographs suggest that there is a degree of cytoskeletal disorganisation in both of these conditions.作者: 驚奇 時間: 2025-3-26 18:17 作者: 你敢命令 時間: 2025-3-26 22:52
An Update on the Hardie Neuroacanthocytosis Seriesfication of several different molecular causes. We have revisited the original Queen Square series in an attempt to correlate the clinical picture and natural history of each case with the new genetic findings.作者: 未完成 時間: 2025-3-27 03:50
Functional Imaging in Neuroacanthocytosistle, but if present appear to be particularly located in the frontal cortex. As with NA, an intriguing variety of devastating movement disorders may arise when specific striatal lesions occur. Due to the low prevalence of NA only a few patients have been investigated to date, and further studies are needed.作者: TOXIN 時間: 2025-3-27 06:58
A Mouse Model of Chorea-Acanthocytosistum. These are thought to be very similar to the features of the disease course and neuropathology seen in ChAc patients. Thus, this model mouse may be useful for pathogenic studies related to ChAc. Here, we review the ChAc-model mouse and recent findings on the upregulation of gephyrin and its related proteins in ChAcmodel mouse striatum.作者: eucalyptus 時間: 2025-3-27 10:56
Neuropathology of Chorea-Acanthocytosission is ubiquitous. Interestingly, additional bands corresponding to proteins of approximately 160 kDa and 94 kDa comprising chorein N-terminal structures appear in brain as well as in several peripheral tissues. Furthermore, chorein is found at a high degree in testis and erythrocytes and at lower levels in muscle.作者: 一起平行 時間: 2025-3-27 15:05 作者: expunge 時間: 2025-3-27 20:58
Update on McLeod Syndromeng studies demonstrate striatal atrophy and subtle cerebral metabolic abnormalities. Neuropathological studies reveal striatal neuronal loss and gliosis without specific features. There is an ongoing search for a suitable animal model to disclose the pathogenetic mechanisms of the disorder and search for possible therapeutic targets.作者: 左右連貫 時間: 2025-3-27 23:58 作者: 通知 時間: 2025-3-28 06:09 作者: Intercept 時間: 2025-3-28 07:19 作者: 要塞 時間: 2025-3-28 11:14 作者: instill 時間: 2025-3-28 14:40
An Update on the Hardie Neuroacanthocytosis Series rare disorder. During the past 15 years, there have been many advances in our understanding of the neuroacanthocytosis syndrome, including the identification of several different molecular causes. We have revisited the original Queen Square series in an attempt to correlate the clinical picture and作者: NAUT 時間: 2025-3-28 20:08 作者: 原始 時間: 2025-3-28 23:46
Huntington’s Disease-Like 2ike HD, HDL2 is characterized by mid-life onset, abnormalities of voluntary and involuntary movement, psychiatric syndromes, and dementia, with a relentless progress to death. The disease is rare, and thus far has only been detected in individuals of African ancestry. Striatal and cortical atrophy i作者: 別炫耀 時間: 2025-3-29 05:46 作者: Alveolar-Bone 時間: 2025-3-29 10:19
The Function of Choreinas three other members: VPS13B, VPS13C and VPS13D. These proteins are similar to Vps13p, a yeast protein shown to be involved in intra-cellular trafficking of a number of transmembrane proteins. Chorein and its homologous human proteins lack domains or motifs of known function. This, together with t作者: athlete’s-foot 時間: 2025-3-29 11:40 作者: 減去 時間: 2025-3-29 18:20
Questions of Cell Shapeis knowledge to the possible pathophysiology underlying the neuroacanthocytosis syndromes. Curvature of animal cell membranes can be induced by a series of different mechanisms: by insertion or deletion of phospholipid from inner or outer leaflet; by contraction or expansion of the underlying cytosk作者: 保守 時間: 2025-3-29 20:31 作者: largesse 時間: 2025-3-29 23:58 作者: GET 時間: 2025-3-30 04:31 作者: 首創(chuàng)精神 時間: 2025-3-30 10:40
Functional Imaging in Neuroacanthocytosisth or without atrophy. There is some evidence that the right side is more affected than the left. Cortical abnormalities are either not present or subtle, but if present appear to be particularly located in the frontal cortex. As with NA, an intriguing variety of devastating movement disorders may a作者: epidermis 時間: 2025-3-30 12:44 作者: cogent 時間: 2025-3-30 20:25
Neuropathology of Chorea-Acanthocytosisrong reactive gliosis and microglial activation, even more distinctive than that found in Huntington’s disease patients. These findings correlate with an impressive macroscopic atrophy of cortical and subcortical structures in ChAc. In Western blot analysis of unaffected brain tissue, chorein expres作者: ordain 時間: 2025-3-30 21:57 作者: TATE 時間: 2025-3-31 02:08 作者: 平項山 時間: 2025-3-31 05:26 作者: ellagic-acid 時間: 2025-3-31 09:40 作者: 繁重 時間: 2025-3-31 13:54 作者: 貴族 時間: 2025-3-31 19:14
S. A. Schneider,R. H. Walker,K. P. Bhatiam is a minimization of the acoustic energy losses in it and of the addition of extraneous reactance, which tends to throw the system out of resonance adjustment. In general, these requirements are met by the mode of attachment in a nodal plane for the angles of twist. The position of this plane (the作者: Critical 時間: 2025-3-31 23:09
