標(biāo)題: Titlebook: Diagnosis and Therapy of Porphyrias and Lead Intoxication; International Sympos Manfred Doss Conference proceedings 1978 Springer-Verlag Be [打印本頁(yè)] 作者: 積聚 時(shí)間: 2025-3-21 16:39
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作者: 刀鋒 時(shí)間: 2025-3-21 23:32
Differential Patterns of Heme and Prophyrin Biosynthesis in Liver and Kidney: Metal Ion Blockade of r the most part, is due to the ready induction response of liver δ-aminolevulinate synthetase (ALAS) — the rate-limiting enzyme of porphyrin-heme synthesis — to the exogenous chemicals and the physiologic factors that alter porphyrin and heme production. Compounds known to be highly potent in alteri作者: 寒冷 時(shí)間: 2025-3-22 01:07 作者: 斜坡 時(shí)間: 2025-3-22 07:49
Permissive Effects of Hormones on the Induction of δ-Aminolevulinic Acid Synthase in Cultured Chick-s enzyme is present in the mitochondria and is inducible in the liver by a variety of compounds of hydrophobic nature. Studies of the regulation of ALA-S have been facilitated by the introduction of a tissue-culture technique for cultivating monolayer of chick-embryo liver cells (2). A major drawbac作者: parasite 時(shí)間: 2025-3-22 11:41 作者: 刪減 時(shí)間: 2025-3-22 14:26
A New Approach to Porphyriaine, has been very helpful for their diagnosis (8). Consecutive biochemical and clinical findings subdivided each group: erythropoietic porphyrias on the basis of different porphyrins occurring in the blood, hepatic porphyrias on the basis of porphyrins and precursors in urine, feces, and liver (8) 作者: 刪減 時(shí)間: 2025-3-22 17:43
The Clinical Chemistry of Variegate Porphyria with Special Reference to the Identification of a New (8), with an estimated incidence of approximately 9000 affected persons. How this remarkable situation has come about has been fully documented by Dean (5) in his monograph, which makes it clear that virtually all South African variegate prophyrics are descendants of a daughter of a marriage that t作者: Glucose 時(shí)間: 2025-3-22 23:54
Expression of the Gene Defects of Acute Intermittent Porphyria (AIP) and Erythropoietic Protoporphyric cells (7) reflects the primary gene defect of AIP, and accounts for the excessive urinary excretion of porphobilinogen and 6-aminolevulinic acid (ALA). The decreased activity of ferrochelatase found in cultured skin fibroblasts and bone-marrow cells from patients with erythropoietic protoporphyri作者: 恭維 時(shí)間: 2025-3-23 04:18 作者: seroma 時(shí)間: 2025-3-23 07:09
A Case of Acute Intermittent Porphyria, Relapsing Acute Pancreatitis, and Unconjugated Hyperbilirubi The previously healthy 36-year-old woman was admitted to the hospital because of severe colicky pain in the right lower abdomen, vomiting, constipation, and red colored urine. A highly increased excretion of porphobilinogen in the urine and a normal fecal excretion of porphyrins was compatible with作者: COLIC 時(shí)間: 2025-3-23 13:34
Acute Intermittent Porphyria; EEG Changes and Their Relationship to the Biochemical Manifestationigations. Stein and Tschudy (9) observed 18 cases of abnormal EEG among 34 patients with AIP in whom an EEG had been recorded. In another investigation of 18 cases (3) almost two-thirds of the patients showed pathologic EEG findings. In what follows we report 8 observations of our own of biochemical作者: acrophobia 時(shí)間: 2025-3-23 15:23 作者: 小卒 時(shí)間: 2025-3-23 20:10 作者: 1FAWN 時(shí)間: 2025-3-24 01:20
Cognitive Capacities and Competencieswith the overall ferrochelatase reaction. To answer these questions, studies were undertaken on the ferrochelatase activity of ultrasonically treated rat liver mitochondria and of tightly coupled rat liver mitochondria.作者: 文件夾 時(shí)間: 2025-3-24 05:02 作者: 懶惰人民 時(shí)間: 2025-3-24 08:48
The Regulatory Function of the Mitochondrial Inner Membrane in the Overall Ferrochelatase Reactionwith the overall ferrochelatase reaction. To answer these questions, studies were undertaken on the ferrochelatase activity of ultrasonically treated rat liver mitochondria and of tightly coupled rat liver mitochondria.作者: malign 時(shí)間: 2025-3-24 14:31
Therapy of Acute Intermittent Porphyria With Ovulation Inhibitors in Womenfore, as a possible cause of acute attacks. Because of the proved inhibition of the secretion of gonadotrophins by combinations of estrogens and gestagens we used ovulation inhibitors for the prophylactic treatment of acute intermittent porphyria.作者: ABIDE 時(shí)間: 2025-3-24 16:06 作者: correspondent 時(shí)間: 2025-3-24 21:46 作者: PRO 時(shí)間: 2025-3-25 02:30 作者: cringe 時(shí)間: 2025-3-25 06:03 作者: hair-bulb 時(shí)間: 2025-3-25 10:57 作者: 文件夾 時(shí)間: 2025-3-25 12:31 作者: FLIRT 時(shí)間: 2025-3-25 16:54 作者: 男生如果明白 時(shí)間: 2025-3-25 23:21 作者: famine 時(shí)間: 2025-3-26 00:38 作者: 細(xì)查 時(shí)間: 2025-3-26 07:48
Sarah Tarlow,Emma Battell Lowman penetrance. The designation ’variegate,1 which was first applied by Barnes and Dean (1) aptly described the various forms that the disease assumes. They are summarized with their percentage incidence in Table 1.作者: 折磨 時(shí)間: 2025-3-26 11:14
Permissive Effects of Hormones on the Induction of δ-Aminolevulinic Acid Synthase in Cultured Chick-mbryo liver cells can be cultivated in a completely chemically defined medium, thus allowing detailed studies on the mechanism of hormone action in these cells. Utilizing this culture method, the permissive effect of insulin, hydrocortisone and triiodothyronine on the induction of ALA-S has been demonstrated.作者: badinage 時(shí)間: 2025-3-26 16:29
The Clinical Chemistry of Variegate Porphyria with Special Reference to the Identification of a New penetrance. The designation ’variegate,1 which was first applied by Barnes and Dean (1) aptly described the various forms that the disease assumes. They are summarized with their percentage incidence in Table 1.作者: accessory 時(shí)間: 2025-3-26 18:54 作者: 明確 時(shí)間: 2025-3-26 21:42 作者: febrile 時(shí)間: 2025-3-27 04:25 作者: 黃瓜 時(shí)間: 2025-3-27 05:50 作者: Focus-Words 時(shí)間: 2025-3-27 10:52
https://doi.org/10.1007/978-3-642-67002-2absorption; anemia; biochemistry; carcinoma; chemistry; diagnosis; diagnostics; differential diagnosis; embr作者: 輕觸 時(shí)間: 2025-3-27 14:52 作者: 褪色 時(shí)間: 2025-3-27 17:46
https://doi.org/10.1007/978-1-137-03641-4Diminished activity of uro-S has been recognized as the primary enzymatic defect in AIP (1, 5, 19). This defect was identified in liver, erythrocytes, and also in other cells. The determination of the enzyme in erythrocytes has proved effective for laboratory medical diagnostics (4–9, 11-18, 20, 21).作者: Gudgeon 時(shí)間: 2025-3-27 22:26
https://doi.org/10.1057/9780230595781Family studies beginning with four patients suffering from AIP were carried out, partly extending to the third generation. The results of the clinical, neurologic, biochemical, and genetic-enzymic investigations are reported and discussed here.作者: 無(wú)王時(shí)期, 時(shí)間: 2025-3-28 03:42
Uroporphyrinogen-Synthase (Uro-S) in Erythrocytes in Acute Intermittent Porphyria (AIP)Diminished activity of uro-S has been recognized as the primary enzymatic defect in AIP (1, 5, 19). This defect was identified in liver, erythrocytes, and also in other cells. The determination of the enzyme in erythrocytes has proved effective for laboratory medical diagnostics (4–9, 11-18, 20, 21).作者: URN 時(shí)間: 2025-3-28 07:27 作者: 值得 時(shí)間: 2025-3-28 11:07 作者: Aggressive 時(shí)間: 2025-3-28 17:09
Shahrukh Rafi Khan,Zeb Rifaqat,Sajid Kazmir the most part, is due to the ready induction response of liver δ-aminolevulinate synthetase (ALAS) — the rate-limiting enzyme of porphyrin-heme synthesis — to the exogenous chemicals and the physiologic factors that alter porphyrin and heme production. Compounds known to be highly potent in alteri作者: 并入 時(shí)間: 2025-3-28 21:05
Cognitive Capacities and Competenciesatase (EC 4.99.1.1,), which is reported to be firmly bound to the inner phase of the mitochondrial inner membrane (2). The topography of the ferrochelatase means that the substrates (iron ions and porphyrinogens) as well as the products (hemes) have to penetrate the mitochondrial inner membrane. Thi作者: Servile 時(shí)間: 2025-3-29 01:13 作者: excrete 時(shí)間: 2025-3-29 04:18
Cognitive Capacities and Competenciesen the acute hepatic porphyrias — namely acute intermittent porphyria (AIP), porphyria variegata (PV), and hereditary coproporphyria (HCP) — there is an uninterrupted biochemical transition. Acute hepatic porphyrias have a series of common features, especially the sensitivity to lipid-soluble drugs,作者: 仔細(xì)閱讀 時(shí)間: 2025-3-29 09:21
Sarah Tarlow,Emma Battell Lowmanine, has been very helpful for their diagnosis (8). Consecutive biochemical and clinical findings subdivided each group: erythropoietic porphyrias on the basis of different porphyrins occurring in the blood, hepatic porphyrias on the basis of porphyrins and precursors in urine, feces, and liver (8) 作者: 起來(lái)了 時(shí)間: 2025-3-29 11:51
Sarah Tarlow,Emma Battell Lowman (8), with an estimated incidence of approximately 9000 affected persons. How this remarkable situation has come about has been fully documented by Dean (5) in his monograph, which makes it clear that virtually all South African variegate prophyrics are descendants of a daughter of a marriage that t作者: 半身雕像 時(shí)間: 2025-3-29 16:01 作者: Concerto 時(shí)間: 2025-3-29 23:03
Bloom, Bardolatry, and Characterolatry IX by decarboxylation and oxidation of two propionyl groups, yielding two vinyl groups (13). Hereditary coproporphyria is a genetic disorder of heme and porphyrin biosynthesis (1). It is inherited as an autosomal dominant and clinically resembles two other forms of genetically transmitted hepatic p作者: Cytokines 時(shí)間: 2025-3-30 02:22
Shakespeare: The Orientation of the Human The previously healthy 36-year-old woman was admitted to the hospital because of severe colicky pain in the right lower abdomen, vomiting, constipation, and red colored urine. A highly increased excretion of porphobilinogen in the urine and a normal fecal excretion of porphyrins was compatible with作者: 掃興 時(shí)間: 2025-3-30 05:40
The Limits of British Influence,igations. Stein and Tschudy (9) observed 18 cases of abnormal EEG among 34 patients with AIP in whom an EEG had been recorded. In another investigation of 18 cases (3) almost two-thirds of the patients showed pathologic EEG findings. In what follows we report 8 observations of our own of biochemical作者: chuckle 時(shí)間: 2025-3-30 08:46 作者: 仔細(xì)檢查 時(shí)間: 2025-3-30 13:31
J?rg Kleff,Sinesio Franco,Martin Lührigized by excessive excretion of porphyrins and their precursors. The prognosis is poor. Patients frequently die due to cessation of respiration after surviving some attacks. Sometimes peripheral pareses occur that do not subside completely. An effective treatment is not yet known. Attacks of acute in
