標(biāo)題: Titlebook: Bone Marrow Failure; Gary M. Kupfer,Gregory H. Reaman,Franklin O. Smith Book 2018 Springer International Publishing AG, part of Springer N [打印本頁] 作者: 倒鉤 時(shí)間: 2025-3-21 19:45
書目名稱Bone Marrow Failure影響因子(影響力)
書目名稱Bone Marrow Failure影響因子(影響力)學(xué)科排名
書目名稱Bone Marrow Failure網(wǎng)絡(luò)公開度
書目名稱Bone Marrow Failure網(wǎng)絡(luò)公開度學(xué)科排名
書目名稱Bone Marrow Failure被引頻次
書目名稱Bone Marrow Failure被引頻次學(xué)科排名
書目名稱Bone Marrow Failure年度引用
書目名稱Bone Marrow Failure年度引用學(xué)科排名
書目名稱Bone Marrow Failure讀者反饋
書目名稱Bone Marrow Failure讀者反饋學(xué)科排名
作者: yohimbine 時(shí)間: 2025-3-21 22:35
Pediatric Oncologyhttp://image.papertrans.cn/b/image/189675.jpg作者: Gnrh670 時(shí)間: 2025-3-22 01:47 作者: 移植 時(shí)間: 2025-3-22 05:27 作者: amorphous 時(shí)間: 2025-3-22 12:25
Bone Marrow Failure978-3-319-61421-2Series ISSN 1613-5318 Series E-ISSN 2191-0812 作者: Flatus 時(shí)間: 2025-3-22 16:33
Literature and Visual Technologiesprogenitor cell. In adult mammals, this process occurs within the bone marrow where hematopoietic progenitors integrate signals and cues from the microenvironment to activate gene expression programs that control lineage specification and maturation. In this chapter, we will review the cellular intr作者: 拋物線 時(shí)間: 2025-3-22 20:40 作者: 輕快走過 時(shí)間: 2025-3-22 22:33 作者: 惹人反感 時(shí)間: 2025-3-23 05:05
Literature and Visual Technologies treatment delivered as multidisciplinary care across several medical and surgical specialties, and lifetime, close monitoring. While bone marrow failure is ultimately treated with bone marrow transplant, continued monitoring for squamous cell carcinoma and other cancer types is crucial due to the m作者: 污點(diǎn) 時(shí)間: 2025-3-23 05:52 作者: Ruptured-Disk 時(shí)間: 2025-3-23 11:24
https://doi.org/10.1057/9780230389991rrow failure (BMF), pulmonary fibrosis, hepatic cirrhosis, and cancer predisposition. Driven by defects in telomere length maintenance, DC is one of a spectrum of telomere biology disorders (TBDs), which includes familial pulmonary fibrosis and the severe variants, Hoyeraal-Hreidarsson syndrome, Rev作者: SUGAR 時(shí)間: 2025-3-23 15:05 作者: BLAND 時(shí)間: 2025-3-23 20:32 作者: Sarcoma 時(shí)間: 2025-3-23 23:24
https://doi.org/10.1007/978-3-031-12330-6lastic anemia is going through an evolution as newer reduced intensity approaches aimed at balancing and minimizing graft failure, graft-versus-host disease (GVHD), and transplant-related morbidity and mortality have resulted in excellent outcomes with limited late effects. Many patients with inheri作者: 閹割 時(shí)間: 2025-3-24 04:44
https://doi.org/10.1007/978-3-031-12330-6 range of proteins involved in granulocytic progenitor expansion, survival, differentiation, cytoskeletal organization, and metabolism. Congenital neutropenias may be associated with non-hematologic abnormalities. While recombinant human granulocyte colony-stimulating factor can improve neutrophil c作者: 絆住 時(shí)間: 2025-3-24 07:13
https://doi.org/10.1007/978-3-031-12330-6patients are usually diagnosed in the newborn period, and they are often mistaken for more common acquired causes of thrombocytopenia. Disorders within this disease group are characterized by ineffective megakaryopoiesis and thrombopoiesis, but vary in their clinical features and causative molecular作者: 多山 時(shí)間: 2025-3-24 13:20
1613-5318 s impacting on understanding of more common hematological an.This book presents the latest scientific knowledge on inherited and acquired bone marrow failure syndromes, describing the advances in understanding of genetics and pathophysiology that have been achieved as a result of high-throughput DNA作者: Cosmopolitan 時(shí)間: 2025-3-24 18:01 作者: Offbeat 時(shí)間: 2025-3-24 20:55
The Cellular and Molecular Mechanisms of Hematopoiesis,oenvironment to activate gene expression programs that control lineage specification and maturation. In this chapter, we will review the cellular intrinsic and extrinsic factors that contribute to the regulation of hematopoiesis in the adult bone marrow.作者: 單色 時(shí)間: 2025-3-25 02:05
Book 2018of genetics and pathophysiology that have been achieved as a result of high-throughput DNA sequencing, RNA expression studies, and modern biochemistry techniques. The full range of relevant conditions is covered, including acquired aplastic anemia, Fanconi anemia, ribosomopathies, telomeropathies, d作者: SOB 時(shí)間: 2025-3-25 04:47 作者: 易達(dá)到 時(shí)間: 2025-3-25 09:52
https://doi.org/10.1007/978-3-031-12330-6s highlighting congenital amegakaryocytic thrombocytopenia (CAMT) and thrombocytopenia absent radius (TAR) as two disorders traditionally classified as inherited bone marrow failure syndromes. Thorough evaluation and accurate diagnosis result in more targeted therapies and appropriate family counseling.作者: prolate 時(shí)間: 2025-3-25 11:50 作者: 和平 時(shí)間: 2025-3-25 16:53 作者: 顧客 時(shí)間: 2025-3-25 21:50
Book 2018ological diseases. A treatment-specific chapter describes options ranging from the conventional to the cutting edge. .Bone Marrow Failure. will be of value for both trainee and practicing hematologists and oncologists..作者: 厭食癥 時(shí)間: 2025-3-26 02:06 作者: Harass 時(shí)間: 2025-3-26 04:47 作者: VAN 時(shí)間: 2025-3-26 08:35
Literature and Visual Technologiesogy of FA, although large gaps in the complete elucidation of the mechanism remain..This chapter reviews the current clinical aspects of FA including presentation, diagnosis, and management, followed by a review of the molecular aspects of FA as they are currently understood.作者: Commission 時(shí)間: 2025-3-26 16:07
https://doi.org/10.1007/978-3-031-12330-6eukemia. Besides serving as a model for understanding bone marrow failure and transformation to myeloid malignancy, these monogenic disorders provide insight into normal cellular and developmental biology of neutrophils and granulopoiesis.作者: In-Situ 時(shí)間: 2025-3-26 17:37 作者: monochromatic 時(shí)間: 2025-3-26 22:59 作者: excrete 時(shí)間: 2025-3-27 01:24
Literature and Visual Technologiess involved in Diamond-Blackfan anemia. The recent finding that several genes affecting ribosome biogenesis are somatically mutated in human tumors implies that understanding the molecular mechanisms underlying this rare group of disorders will likely have much broader implications.作者: intrigue 時(shí)間: 2025-3-27 08:34
https://doi.org/10.1007/978-3-031-12330-6syndrome (.) gene. SBDS functions in ribosomal biogenesis as well as other cellular processes. In this chapter we will summarize clinical manifestations of SDS and diagnostic and treatment approaches, as well as highlight novel advances in the understanding of the molecular pathogenesis of SDS.作者: 勛章 時(shí)間: 2025-3-27 11:17 作者: 制定法律 時(shí)間: 2025-3-27 14:21
Gertrude Stein’s Machinery of Perceptionand supportive care. Advances in gene discovery and genetic diagnostic techniques have shown that as many as 20–30% of patients previously thought to have idiopathic AA actually have an underlying genetic cause, making it clear that extending genetic testing beyond basic screening is of paramount im作者: Vital-Signs 時(shí)間: 2025-3-27 19:55 作者: 范圍廣 時(shí)間: 2025-3-28 00:03 作者: 不可救藥 時(shí)間: 2025-3-28 04:21
https://doi.org/10.1007/978-3-031-12330-6transplantation in severe aplastic anemia, Fanconi anemia, dyskeratosis congenita, Diamond-Blackfan anemia, Shwachman-Diamond syndrome, severe congenital neutropenia, and congenital amegakaryocytic thrombocytopenia. The forthcoming role of gene therapy is also discussed.作者: 食道 時(shí)間: 2025-3-28 06:40
Acquired Aplastic Anemia,and supportive care. Advances in gene discovery and genetic diagnostic techniques have shown that as many as 20–30% of patients previously thought to have idiopathic AA actually have an underlying genetic cause, making it clear that extending genetic testing beyond basic screening is of paramount im作者: engagement 時(shí)間: 2025-3-28 12:21 作者: 純樸 時(shí)間: 2025-3-28 17:50
Diamond-Blackfan Anemia,rogress using zebrafish and mouse models of DBA has advanced our understanding of the role of nucleolar stress (p53-dependent) and p53-independent mechanisms in the development of the DBA phenotype, providing strategies for therapeutic intervention. DBA is also confirmed to be a cancer predispositio作者: genesis 時(shí)間: 2025-3-28 21:10
Hematopoietic Cell Transplantation for the Treatment of Patients with Bone Marrow Failure Syndromestransplantation in severe aplastic anemia, Fanconi anemia, dyskeratosis congenita, Diamond-Blackfan anemia, Shwachman-Diamond syndrome, severe congenital neutropenia, and congenital amegakaryocytic thrombocytopenia. The forthcoming role of gene therapy is also discussed.作者: AGATE 時(shí)間: 2025-3-29 00:56 作者: 云狀 時(shí)間: 2025-3-29 05:05
Acquired Aplastic Anemia, majority of cases, hence the term idiopathic aplastic anemia. The major pathophysiologic mechanism implicated in acquired AA is autoimmune dysregulation resulting in damage to hematopoietic stem and progenitor cells. Hematopoietic stem cell transplantation (HSCT) from a human leukocyte antigen matc作者: 混合,攙雜 時(shí)間: 2025-3-29 09:45
Pediatric Myelodysplastic Syndromes,topoiesis with high risk for leukemic transformation to acute myeloid leukemia. The clinical, laboratory, and histologic presentation of pediatric MDS shares significant overlap with inherited and acquired bone marrow failure disorders, which makes the diagnosis challenging. Definitive diagnosis of 作者: Etymology 時(shí)間: 2025-3-29 15:14
Fanconi Anemia: A Pathway of Hematopoiesis and Cancer Predisposition, treatment delivered as multidisciplinary care across several medical and surgical specialties, and lifetime, close monitoring. While bone marrow failure is ultimately treated with bone marrow transplant, continued monitoring for squamous cell carcinoma and other cancer types is crucial due to the m作者: 果核 時(shí)間: 2025-3-29 18:35
Ribosomopathies Through a Diamond Lens,typical ribosomopathy, Diamond-Blackfan anemia, to explore relationships between the structure of the ribosome, its biogenesis, and the molecular mechanisms that contribute to disease pathology. Other ribosomopathies are discussed as they relate to the genes affected and pathophysiological mechanism