標題: Titlebook: Blistering Diseases; Clinical Features, P Dédée F. Murrell Book 2015 Springer-Verlag Berlin Heidelberg 2015 Epidermolysis bullosa.Immunoflu [打印本頁] 作者: digestive-tract 時間: 2025-3-21 19:26
書目名稱Blistering Diseases影響因子(影響力)
書目名稱Blistering Diseases影響因子(影響力)學(xué)科排名
書目名稱Blistering Diseases網(wǎng)絡(luò)公開度
書目名稱Blistering Diseases網(wǎng)絡(luò)公開度學(xué)科排名
書目名稱Blistering Diseases被引頻次
書目名稱Blistering Diseases被引頻次學(xué)科排名
書目名稱Blistering Diseases年度引用
書目名稱Blistering Diseases年度引用學(xué)科排名
書目名稱Blistering Diseases讀者反饋
書目名稱Blistering Diseases讀者反饋學(xué)科排名
作者: CRAMP 時間: 2025-3-21 22:02
The Immune System in Normal Skin and in AIBDnment, it protects against hazardous substances, such as chemicals and physical stress. Various immune cells reside in the two main compartments of the skin, the epidermis and the dermis, under physiological steady-state conditions. It is essential for maintaining the integrity of the skin that immu作者: 斑駁 時間: 2025-3-22 02:09 作者: 飛行員 時間: 2025-3-22 07:51 作者: 不能根除 時間: 2025-3-22 11:09
Desmosomal Proteins as Autoantigens in Pemphigusere are several variants of pemphigus, each with unique clinical, histological, and immunologic features. Interestingly, when different desmosomal proteins are targeted by the autoimmune response, different clinical and histological features are seen. In this chapter we review the key intercellular 作者: 有節(jié)制 時間: 2025-3-22 14:22
Collagen XVII and Its Role in Junctional Epidermolysis Bullosathelial cells to the underlying basement membrane. It is a homotrimeric type II transmembrane protein consisting of three 180 kDa alpha-1 (XVII) chains. Each individual chain is encoded by the . gene. Mutations in . usually lead to loss of collagen XVII and a phenotype comprising congenital generali作者: Freeze 時間: 2025-3-22 19:21 作者: 星星 時間: 2025-3-22 21:13 作者: 爭吵加 時間: 2025-3-23 05:04 作者: 偶然 時間: 2025-3-23 06:46
Kindlin-1 and Its Role in Kindler Syndromedhesions, which serve as supramolecular signalling and actin-anchoring platforms. Together with talin, kindlins directly bind to integrin β subunit cytoplasmic tails and are responsible for integrin activation. Mutations in the kindlin-1 gene cause the Kindler syndrome, a rare genodermatosis charact作者: 偽書 時間: 2025-3-23 09:44 作者: Hectic 時間: 2025-3-23 17:05 作者: grounded 時間: 2025-3-23 21:57 作者: BOLUS 時間: 2025-3-24 00:11
Apoptosis and Signaling in Bullous Diseases: Pemphiguss (acantholysis). By an as yet unknown mechanism, autoantibodies are produced and bind to keratinocyte proteins. The best characterized pemphigus autoantigens are the desmosome cadherins desmoglein 3 and desmoglein 1. Pemphigus autoantibodies are pathogenic; passive transfer of dsg1 and dsg3 IgG aut作者: entice 時間: 2025-3-24 05:03
How to Take a Skin Biopsy Correctly to Diagnose Epidermolysis Bullosa and Autoimmune Bullous Diseaseppropriate clinical setting with routine histology consistent wtih an AIBD. Diagnostic modalities for epidermolysis bullosa (EB) include immunofluorescence antigenic mapping (IFM), transmission electron microscopy (TEM), and genetic mutational analysis. Of these, the most preferred is IFM. Because a作者: 性滿足 時間: 2025-3-24 07:40 作者: Mediocre 時間: 2025-3-24 14:06
ELISA Testing and Immunoblottingsts, enzyme-linked immunosorbent assay (ELISA) and immunoblotting are now two major methods to diagnose autoimmune bullous diseases. Two major groups of autoimmune bullous disease are pemphigus and pemphigoid. The major autoantigens of pemphigus are desmogleins, and those of pemphigoid are BP180 and作者: 變白 時間: 2025-3-24 16:09
Book 2015g of the pathogenetic mechanisms to management of the individual diseases. The aim is to provide a detailed reference for dermatologists who care for patients with these conditions and a useful “one-stop information shop” for specialists outside of dermatology. The book opens by describing the struc作者: Rinne-Test 時間: 2025-3-24 21:16 作者: BROTH 時間: 2025-3-25 02:52 作者: 過分 時間: 2025-3-25 07:21 作者: 手術(shù)刀 時間: 2025-3-25 11:03 作者: 委托 時間: 2025-3-25 13:19 作者: Militia 時間: 2025-3-25 17:11
?ffentlicher Raum als privater Bildungsraum in the current classification of EB: plakophilin-1, desmoplakin and plakoglobin. It is possible that future classifications of EB will be expanded to include additional desmosomal genodermatoses in which there is also skin fragility and erosions.作者: 鍵琴 時間: 2025-3-25 21:20 作者: Offensive 時間: 2025-3-26 03:17
Lernstile im interkulturellen Kontextma]1 pemphigoid, and linear IgA bullous dermatosis, are made by a combination of ELISA and immunoblotting using various substrates, including normal human epidermal and dermal extracts, recombinant proteins of NC16a and C-terminal domains of BP180, purified human laminin-332, and concentrated HaCaT cell culture supernatant.作者: Dri727 時間: 2025-3-26 04:42 作者: Antimicrobial 時間: 2025-3-26 08:41 作者: Ruptured-Disk 時間: 2025-3-26 13:50
Pathogenesis of Epidermolysis Bullosa Acquisitad Fc gamma receptor-dependent activation of effector leukocytes. Inflammatory mediators, released by these cells, including reactive oxygen species and proteolytic enzymes, finally induce dermal-epidermal separation.作者: 令人心醉 時間: 2025-3-26 20:01 作者: offense 時間: 2025-3-27 00:16
Book 2015ality illustrations. The forms of treatment appropriate in specific conditions are then described in depth, with coverage of dressings, drugs, surgical procedures, gene therapy, and other novel approaches. Helpful algorithms are included both for testing and monitoring and for treatment.作者: 審問,審訊 時間: 2025-3-27 03:02
cludes algorithms for treatment and for testing and monitoriThis book is a comprehensive compendium of current knowledge on inherited and autoimmune blistering diseases that relates advances in our understanding of the pathogenetic mechanisms to management of the individual diseases. The aim is to p作者: 言行自由 時間: 2025-3-27 06:26 作者: facilitate 時間: 2025-3-27 12:46
Franziska Schmithüsen,Dieter Ferring densa zone at the level of AF. DEB results from different mutations in the type VII collagen gene (.). The nature of mutations in . and their positions correlate reasonably logically with the severity of the resulting phenotypes of dystrophic EB.作者: 女歌星 時間: 2025-3-27 14:19
Integrins A6 and B4 and Their Role in Junctional Epidermolysis Bullosa and Recessive Epidermolysis Bese genes or other factors. From the mutation database in ITGA6 and ITGB4, there is a predominance of premature termination codon (PTC) mutations in the lethal forms, whereas missense and PTC mutations share the nonlethal variant and missense/missense mutations cause different clinical variants.作者: IDEAS 時間: 2025-3-27 20:32
COL7A1 and Its Role in Dystrophic Epidermolysis Bullosa densa zone at the level of AF. DEB results from different mutations in the type VII collagen gene (.). The nature of mutations in . and their positions correlate reasonably logically with the severity of the resulting phenotypes of dystrophic EB.作者: 小平面 時間: 2025-3-28 01:40
Design und Auswertung einer Anwendungsstudient membrane, whether through inherited genetic mutations or acquired autoimmune disorders, results in disruption of dermal-epidermal cohesion and blistering disease. The dermal-epidermal basement membrane also plays a key role in dynamic processes such as skin development, carcinoma invasion, and wound healing.作者: BLANC 時間: 2025-3-28 04:05 作者: 生銹 時間: 2025-3-28 09:51
Lernstile im interkulturellen Kontextntly, the first non-HLA genes have been associated with pemphigus vulgaris. In pemphigus vulgaris and foliaceus, the potential impact drugs, smoking and vaccination have been described, while in the endemic forms of pemphigus foliaceus, the role of environmental factors, including infectious agents, is emerging.作者: 小卷發(fā) 時間: 2025-3-28 11:03 作者: DRAFT 時間: 2025-3-28 15:21 作者: coagulation 時間: 2025-3-28 22:28 作者: 放牧 時間: 2025-3-28 23:02 作者: acetylcholine 時間: 2025-3-29 05:07 作者: 描述 時間: 2025-3-29 11:07
Design und Auswertung einer Anwendungsstudieclude specialized laminins, collagens, integrins, as well as other unique structural components which together serve to connect the intermediate filament network of the basal keratinocyte cytoskeleton to the interstitial collagen network of the papillary dermis. Damage to the dermal-epidermal baseme作者: charisma 時間: 2025-3-29 12:15 作者: pacific 時間: 2025-3-29 16:11
Design und Auswertung einer Anwendungsstudieave been shown to regulate additional biological processes of importance such as protein synthesis, cell migration, and apoptosis. Much of this knowledge has been gained through the study of rare disorders, known as keratinopathies, which are caused by mutations in genes encoding the various epiderm作者: 標準 時間: 2025-3-29 22:45
?ffentlicher Raum als privater Bildungsraumosome anchoring complexes. Over the last few years, however, the clinicopathological spectrum of EB has been expanded to also include primary abnormalities in desmosome junctions. Desmosomes are intercellular junctions that contribute to cell-cell adhesion, signalling, development and differentiatio作者: intrude 時間: 2025-3-30 03:53
Wolfgang Wittwer,Andreas Diettrichere are several variants of pemphigus, each with unique clinical, histological, and immunologic features. Interestingly, when different desmosomal proteins are targeted by the autoimmune response, different clinical and histological features are seen. In this chapter we review the key intercellular 作者: Toxoid-Vaccines 時間: 2025-3-30 04:50
Wolfgang Wittwer,Andreas Diettrichthelial cells to the underlying basement membrane. It is a homotrimeric type II transmembrane protein consisting of three 180 kDa alpha-1 (XVII) chains. Each individual chain is encoded by the . gene. Mutations in . usually lead to loss of collagen XVII and a phenotype comprising congenital generali作者: 向外 時間: 2025-3-30 08:22 作者: landmark 時間: 2025-3-30 15:57 作者: 壕溝 時間: 2025-3-30 20:22 作者: 費解 時間: 2025-3-30 21:59
Franziska Schmithüsen,Fernand Antondhesions, which serve as supramolecular signalling and actin-anchoring platforms. Together with talin, kindlins directly bind to integrin β subunit cytoplasmic tails and are responsible for integrin activation. Mutations in the kindlin-1 gene cause the Kindler syndrome, a rare genodermatosis charact作者: Irrepressible 時間: 2025-3-31 03:43
Franziska Schmithüsen,Dieter Ferringhe collagen VII gene (COL7A1). Dystrophic epidermolysis bullosa (DEB) is an inherited skin fragility disorder, and blistering occurs in the sub-lamina densa zone at the level of AF. DEB results from different mutations in the type VII collagen gene (.). The nature of mutations in . and their positio作者: Extort 時間: 2025-3-31 07:46 作者: Ingenuity 時間: 2025-3-31 10:54
Lernstile im interkulturellen Kontextalso with regard to genetic and environmental predisposing factors. A strong association with HLA alleles was found in pemphigus, mucous membrane pemphigoid, pemphigoid gestationis and epidermolysis bullosa acquisita, whereas in bullous pemphigoid, this association appeared much less prominent. Rece作者: breadth 時間: 2025-3-31 13:47 作者: Substitution 時間: 2025-3-31 18:23
Lernstile im interkulturellen Kontextppropriate clinical setting with routine histology consistent wtih an AIBD. Diagnostic modalities for epidermolysis bullosa (EB) include immunofluorescence antigenic mapping (IFM), transmission electron microscopy (TEM), and genetic mutational analysis. Of these, the most preferred is IFM. Because a
