標題: Titlebook: Auto-Inflammatory Syndromes; Pathophysiology, Dia Petros Efthimiou Book 2019 Springer Nature Switzerland AG 2019 auto-inflammatory syndrome [打印本頁] 作者: 搖尾乞憐 時間: 2025-3-21 16:13
書目名稱Auto-Inflammatory Syndromes影響因子(影響力)
書目名稱Auto-Inflammatory Syndromes影響因子(影響力)學科排名
書目名稱Auto-Inflammatory Syndromes網(wǎng)絡公開度
書目名稱Auto-Inflammatory Syndromes網(wǎng)絡公開度學科排名
書目名稱Auto-Inflammatory Syndromes被引頻次
書目名稱Auto-Inflammatory Syndromes被引頻次學科排名
書目名稱Auto-Inflammatory Syndromes年度引用
書目名稱Auto-Inflammatory Syndromes年度引用學科排名
書目名稱Auto-Inflammatory Syndromes讀者反饋
書目名稱Auto-Inflammatory Syndromes讀者反饋學科排名
作者: 遺忘 時間: 2025-3-21 22:40
Background on Computational Complexitytacks..New treatment modalities have been developed based on recent advances in pathogenesis of MKD/HIDS. Stemming from the proposed mechanism of inflammasome activation, IL-1 pathway appears to be the most effective therapeutic target to date..Early diagnosis and treatment are crucial in MKD/HIDS a作者: 手勢 時間: 2025-3-22 02:03
Asymptotically Dominant Properties, hyperinflammatory stages called macrophage activation syndrome, a form of reactive hemophagocytic lymphohistiocytosis, which may occur in 50% of patients but become clinically overt only in a smaller proportion. Multidisciplinary teams are best fit to treat this complex disease. Decades after nonb作者: pacifist 時間: 2025-3-22 05:46 作者: 圓木可阻礙 時間: 2025-3-22 11:15
ment plans, and advice on how to best transition pediatric patients into adult treatment. This is an invaluable reference on auto-inflammatory syndromes for clinicians and researchers in pediatric and adult rheumatology and immunology..978-3-319-96929-9作者: BLANK 時間: 2025-3-22 15:19
Immunology of Auto-inflammatory Syndromes,omain (NOD) proteins and the NOD-like receptors (NLRs), which serve as key mediators in both innate immunity and autoinflammation largely through ability to form inflammasomes. Indeed, many autoinflammatory disorders converge at the level of inflammasome activation. Inflammasomes and other sensors t作者: metropolitan 時間: 2025-3-22 18:00 作者: 熱烈的歡迎 時間: 2025-3-23 00:38
Systemic Juvenile Idiopathic Arthritis, hyperinflammatory stages called macrophage activation syndrome, a form of reactive hemophagocytic lymphohistiocytosis, which may occur in 50% of patients but become clinically overt only in a smaller proportion. Multidisciplinary teams are best fit to treat this complex disease. Decades after nonb作者: Morphine 時間: 2025-3-23 02:31 作者: 忍受 時間: 2025-3-23 09:31 作者: CAND 時間: 2025-3-23 11:26
Deficiency of the Interleukin-36 Receptor Antagonist (DITRA) and Generalized Pustular Psoriasistor antagonist . locus. The mutations encode for an unstable protein with poor interaction with its receptor allowing for an unopposed effect of IL-36 that results in enhanced production of pro-inflammatory cytokines and systemic inflammation.作者: Demonstrate 時間: 2025-3-23 14:41
Book 2019ease presentations, and clinical treatment guidelines. The book is divided into two sections, adult and pediatric, with chapters focusing on individuals diseases such as systemic arthritis, hyper-IgD, pap syndrome, idiopathic recurrent pericarditis, and familial Mediterranean fever. Chapters incorpo作者: 開玩笑 時間: 2025-3-23 18:51
gy of these diseases to inform clinical decision making.Cove.This book provides an overview of auto-inflammatory syndromes, covering the underlying immune mechanisms that lead to their development, specific disease presentations, and clinical treatment guidelines. The book is divided into two sectio作者: Devastate 時間: 2025-3-23 23:10
Background on Combinatorial Group Theoryancestry but has been described in almost all ethnic groups, including those living in Mediterranean countries and Asia. Fever is often prolonged and can be accompanied by serositis, arthritis, a skin rash with underlying fasciitis and periorbital oedema.作者: Cholagogue 時間: 2025-3-24 02:29 作者: 座右銘 時間: 2025-3-24 07:10 作者: 小卷發(fā) 時間: 2025-3-24 10:55
The TNF Receptor-Associated Autoinflammatory Syndrome (TRAPS)ancestry but has been described in almost all ethnic groups, including those living in Mediterranean countries and Asia. Fever is often prolonged and can be accompanied by serositis, arthritis, a skin rash with underlying fasciitis and periorbital oedema.作者: CLIFF 時間: 2025-3-24 17:25
Blau Syndromeis characterized predominantly by granulomas in the affected areas. Management remains a challenge, as Blau syndrome is rare and evidence is lacking. Here, we describe in greater detail the clinical features, pathophysiology, diagnosis, management, and prognosis of Blau syndrome.作者: 精密 時間: 2025-3-24 20:54
Cryopyrin-Associated Periodic Syndromes (CAPS)ral hearing loss, renal failure, hydrocephalus, and skeletal deformities. International efforts have advanced our understanding of the disease mechanisms. Through partnerships we dramatically increased our ability to rapidly diagnose CAPS, select optimal therapies, monitor disease activity, and prevent damage accrual.作者: occurrence 時間: 2025-3-25 03:12 作者: Lasting 時間: 2025-3-25 07:00
Background on Public Key Cryptography 25% mortality. Long-term sequelae include joint contractures and deformities, muscle atrophy, growth retardation, and developmental delay. The disease is highly and rapidly responsive to IL-1 blockade.作者: TIA742 時間: 2025-3-25 11:35
Background on Combinatorial Group Theory development of amyloidosis which is the most significant complication of FMF. However, a minor proportion of patients can be resistant to colchicine. If colchicine fails, anti-IL-1 therapy is a promising second-line therapy.作者: 幼稚 時間: 2025-3-25 14:43 作者: 關心 時間: 2025-3-25 18:22 作者: 討好女人 時間: 2025-3-25 20:02
PAPA Syndrome and the Spectrum of PSTPIP1-Associated Inflammatory Diseasesof the endogenous TLR4 agonists myeloid-related proteins (MRP) 8 and 14 are characteristic features of these diseases and might play a central role in the pathogenesis..Here, we give an overview about the expanding spectrum of autoinflammatory diseases due to mutations in . and insights into their pathogenesis.作者: 不能妥協(xié) 時間: 2025-3-26 02:46 作者: GOUGE 時間: 2025-3-26 06:01 作者: 黃油沒有 時間: 2025-3-26 10:18 作者: Intruder 時間: 2025-3-26 16:30
Chronic Nonbacterial Osteomyelitists develop complications before “matching” treatment has been established. Here, we discuss disease presentation and outcomes, the current understanding of disease pathology, diagnostic approaches to CNO, available treatment options, and potential future directions.作者: malapropism 時間: 2025-3-26 17:25
Book 2019ory disorders to offer detailed clinical guidelines regarding diagnostic techniques, treatment plans, and advice on how to best transition pediatric patients into adult treatment. This is an invaluable reference on auto-inflammatory syndromes for clinicians and researchers in pediatric and adult rheumatology and immunology..作者: Pantry 時間: 2025-3-26 23:16
Background on Computational Complexitytial lung disease, and growth retardation are among the most common features shared by the majority of type I interferonopathies. Targeting of type I IFN signaling seems to hold a promising therapeutic role.作者: Organonitrile 時間: 2025-3-27 03:56
Generic Complexity of NP-complete Problemsng “cytokine storm,” and there is significant morbidity and mortality associated with it. Aggressive treatment with high-dose intravenous corticosteroids, immunomodulators, antineoplastic agents, and, depending on the underlying etiology, biologics is necessary to prevent organ damage and improve survival.作者: 輕打 時間: 2025-3-27 08:59
Length-Based and Quotient Attacksurrently, there is no approved treatment for the Schnitzler syndrome. Interleukin-1 blocking agents seem to be the most effective therapies, even though only on the inflammation-linked symptoms, not on the monoclonal component.作者: 確定 時間: 2025-3-27 13:17 作者: 否認 時間: 2025-3-27 17:15
Macrophage Activation Syndrome (MAS)ng “cytokine storm,” and there is significant morbidity and mortality associated with it. Aggressive treatment with high-dose intravenous corticosteroids, immunomodulators, antineoplastic agents, and, depending on the underlying etiology, biologics is necessary to prevent organ damage and improve survival.作者: kindred 時間: 2025-3-27 18:51
Schnitzler Syndromeurrently, there is no approved treatment for the Schnitzler syndrome. Interleukin-1 blocking agents seem to be the most effective therapies, even though only on the inflammation-linked symptoms, not on the monoclonal component.作者: 彩色 時間: 2025-3-28 00:02
Length-Based and Quotient Attacksf innate immunity are host germline-encoded pattern recognition receptors, which sense conserved structural features present on pathogens or signs of tissue damage, and trigger production of inflammatory responses. In contrast, autoinflammation represents a disordered and inappropriate innate immune作者: 結合 時間: 2025-3-28 06:01
Background on Computational ComplexityIDS patients most commonly present with recurrent febrile attacks, gastrointestinal symptoms (abdominal pain, nausea, and vomiting), inflammatory arthritis, and arthralgia as well as mucocutaneous manifestations. Disease usually manifests in childhood, although adult cases of HIDS have been describe作者: Facilities 時間: 2025-3-28 09:10 作者: 壓倒 時間: 2025-3-28 12:45 作者: 進入 時間: 2025-3-28 17:45 作者: bromide 時間: 2025-3-28 20:13 作者: 偽造者 時間: 2025-3-29 02:07 作者: MAIZE 時間: 2025-3-29 05:11
Length-Based and Quotient Attacksxcess secretion of interleukin 1. CAPS is characterized by systemic and organ inflammation baring the risk of irreversible damage including sensorineural hearing loss, renal failure, hydrocephalus, and skeletal deformities. International efforts have advanced our understanding of the disease mechani作者: 不滿分子 時間: 2025-3-29 09:27 作者: 潛移默化 時間: 2025-3-29 15:21
Background on Computational Complexitytion of endogenous nucleic acids, excessive sensitivity or activity of DNA/RNA sensors, and the dysregulation of type I IFN pathway have been identified as the main contributors to excessive type I IFN signaling in this setting. Chilblain-like lesions, central nervous system calcifications, intersti作者: 微粒 時間: 2025-3-29 17:44 作者: COUCH 時間: 2025-3-29 23:24
Background on Combinatorial Group Theorymatory disease characterized by periodic fever, dermatitis, arthritis, and swelling of the distal extremities, as well as gastrointestinal and sicca-like symptoms. The disorder is associated with specific . variants.作者: BAIL 時間: 2025-3-30 03:14
Asymptotically Dominant Propertiesiven condition characterized by chronic, multiorganic inflammatory involvement. Typical clinical features including young age at presentation, fever, neutrophilic skin lesions, synovitis, serositis, organomegaly, as well as increased risk of amyloidosis are reminiscent of (and may mimic) certain mon作者: Herpetologist 時間: 2025-3-30 06:36 作者: 結構 時間: 2025-3-30 09:38 作者: 做作 時間: 2025-3-30 12:32 作者: LATER 時間: 2025-3-30 17:33 作者: 問到了燒瓶 時間: 2025-3-30 23:01 作者: 胰臟 時間: 2025-3-31 04:33
Petros EfthimiouProvides thorough, up-to-date information and clinical applications for auto-inflammatory syndromes.Includes basic science and pathophysiology of these diseases to inform clinical decision making.Cove作者: outset 時間: 2025-3-31 07:25
http://image.papertrans.cn/b/image/166076.jpg作者: 不舒服 時間: 2025-3-31 12:19
Yao Syndromematory disease characterized by periodic fever, dermatitis, arthritis, and swelling of the distal extremities, as well as gastrointestinal and sicca-like symptoms. The disorder is associated with specific . variants.作者: watertight, 時間: 2025-3-31 13:24 作者: 使害羞 時間: 2025-3-31 19:20
Springer Nature Switzerland AG 2019作者: 憤怒事實 時間: 2025-3-31 22:43 作者: Jingoism 時間: 2025-4-1 03:43
Mevalonate Kinase Deficiency (MKD)/Hyperimmunoglobulin D Syndrome (HIDS)IDS patients most commonly present with recurrent febrile attacks, gastrointestinal symptoms (abdominal pain, nausea, and vomiting), inflammatory arthritis, and arthralgia as well as mucocutaneous manifestations. Disease usually manifests in childhood, although adult cases of HIDS have been describe
